Informazioni generali
  • Categoria della malattia Malattie genetiche , Malattie delle vie respiratorie (non cancro) (BASEC)
  • Stato di reclutamento reclutamento in corso (BASEC/ICTRP)
  • Luogo dello studio
    Berna, Zurigo
    (BASEC)
  • Responsabile dello studio Prof. Dr. Alexander Möller alexander.moeller@kispi.uzh.ch (BASEC)
  • Fonte dati BASEC: Importato da 10.06.2025 ICTRP: N/A
  • Ultimo aggiornamento 10.06.2025 17:35
HumRes66010 | SNCTP000006162 | BASEC2024-01598

An extension study to assess the long-term safety and efficacy of a triple combination therapy of Elexacaftor/Tezacaftor/Ivacaftor (ELX/TEZ/IVA) in children with cystic fibrosis who are at least 1 year old.

  • Categoria della malattia Malattie genetiche , Malattie delle vie respiratorie (non cancro) (BASEC)
  • Stato di reclutamento reclutamento in corso (BASEC/ICTRP)
  • Luogo dello studio
    Berna, Zurigo
    (BASEC)
  • Responsabile dello studio Prof. Dr. Alexander Möller alexander.moeller@kispi.uzh.ch (BASEC)
  • Fonte dati BASEC: Importato da 10.06.2025 ICTRP: N/A
  • Ultimo aggiornamento 10.06.2025 17:35

Descrizione riassuntiva dello studio

The aim of this extension study (VX22-445-123) is to assess the long-term safety and efficacy of a triple combination therapy of Elexacaftor/Tezacaftor/Ivacaftor (ELX/TEZ/IVA) in children with cystic fibrosis who are at least 1 year old. Participation in this study lasts just under two years. All participants receive the investigational drug, and both the parents/legal guardians of the participating children and the investigator know the administered dose. The insights gained from this study may be helpful in the future for the treatment of cystic fibrosis or other diseases and deepen scientific understanding.

(BASEC)

Intervento studiato

In this study, the term "investigational drug" refers to the triple combination of Elexacaftor/Tezacaftor/Ivacaftor (ELX/TEZ/IVA). ELX/TEZ/IVA is approved in some countries for use in certain patients with cystic fibrosis, and the researchers believe it may also be beneficial for younger age groups.

Even though the investigational drug was used in the main study (VX22-445-122), it is considered an investigational drug for this age group, meaning it has not yet been approved by some health authorities and is still being studied regarding long-term safety and efficacy for patients in this age group.

Participants in this study will receive one of four possible doses of the investigational drug based on their body weight. The dose may be adjusted if body weight changes during the treatment period.

Participation in the study lasts approximately 100 weeks (up to 96 weeks for the study treatment period and up to 4 weeks for the safety follow-up period).

Overall, participants, accompanied by parents, will come to the clinic at least 11 times over a period of 23 months. A study visit may last from 30 minutes to 4 hours. After 25 months, participation in the study is completed.

(BASEC)

Malattie studiate

This study (extension study, VX22-445-123) targets children who are at least 1 year old, suffer from cystic fibrosis, and have participated in the main study (VX22-445-122).

(BASEC)

Criteri di partecipazione
1. The parents or legal guardian of the participating child have signed an informed consent form to participate. 2. At the discretion of the investigator, the parents or guardian must be able to understand the study requirements, restrictions, and instructions, and ensure that the child adheres to the study requirements and that the study is likely to be completed as planned. 3. The informed consent form was not revoked for the main study (VX22-445-122). (BASEC)

Criteri di esclusione
1. A disease or clinical condition has occurred in the participating child that could distort the study results or pose an additional risk during the administration of the investigational drug(s), such as liver cirrhosis, solid organ or hematological transplantation, cancer. 2. A drug intolerance occurred in the participating child in the main study VX22-445-122 that would expose the participating child to an additional risk. 3. Current participation in another clinical study other than the main study VX22-445-122. 4. Poor adherence to the investigational drug and/or does not follow the procedures in the main study VX22-445-122 according to the investigator's opinion. (BASEC)

Luogo dello studio

Berna, Zurigo

(BASEC)

non disponibile

Sponsor

Vertex Pharmaceuticals (CH) GmbH

(BASEC)

Contatto per ulteriori informazioni sullo studio

Persona di contatto in Svizzera

Prof. Dr. Alexander Möller

+41442667079

alexander.moeller@kispi.uzh.ch

Universitäts-Kinderspital Zürich, Pädiatrie, pädiatrische Pneumologie, Schlafmedizin (SSSSC)

(BASEC)

Informazioni scientifiche

non disponibile

Nome del comitato etico approvante (per studi multicentrici solo il comitato principale)

Commissione etica Zurigo

(BASEC)

Data di approvazione del comitato etico

29.10.2024

(BASEC)


ID di studio ICTRP
non disponibile

Titolo ufficiale (approvato dal comitato etico)
Eine offene Phase-III-Studie zur Beurteilung der Langzeitsicherheit und -wirksamkeit von Elexacaftor/Tezacaftor/Ivacaftor bei Mukoviszidose-Patienten ab 12 Monaten (BASEC)

Titolo accademico
non disponibile

Titolo pubblico
non disponibile

Malattie studiate
non disponibile

Intervento studiato
non disponibile

Tipo di studio
non disponibile

Disegno dello studio
non disponibile

Criteri di inclusione/esclusione
non disponibile

non disponibile

Endpoint primari e secondari
non disponibile

non disponibile

Data di registrazione
non disponibile

Inclusione del primo partecipante
non disponibile

Sponsor secondari
non disponibile

Contatti aggiuntivi
non disponibile

ID secondari
non disponibile

Risultati-Dati individuali dei partecipanti
non disponibile

Ulteriori informazioni sullo studio
non disponibile

Risultati dello studio

Riepilogo dei risultati

non disponibile

Link ai risultati nel registro primario

non disponibile