General information
  • Disease category Nutritional and Metabolic diseases (BASEC)
  • Study Phase N/A (ICTRP)
  • Recruitment status recruitment ongoing (BASEC/ICTRP)
  • Trial sites
    Zurich
    (BASEC)
  • Contact Johannes Häberle johannes.haeberle@kispi.uzh.ch (BASEC)
  • Data Source(s) BASEC: Import from 04.07.2025 ICTRP: Import from 12.04.2025
  • Last update 04.07.2025 08:56
HumRes50165 | SNCTP000003803 | BASEC2019-01352 | NCT05671666

Ureagenesis Analysis

  • Disease category Nutritional and Metabolic diseases (BASEC)
  • Study Phase N/A (ICTRP)
  • Recruitment status recruitment ongoing (BASEC/ICTRP)
  • Trial sites
    Zurich
    (BASEC)
  • Contact Johannes Häberle johannes.haeberle@kispi.uzh.ch (BASEC)
  • Data Source(s) BASEC: Import from 04.07.2025 ICTRP: Import from 12.04.2025
  • Last update 04.07.2025 08:56

Summary description of the study

The project concerns the introduction of a new test. This is intended to examine the function of the urea cycle and be more accurate than previous methods. The test takes several hours and requires drinking a salty solution, followed by several blood draws from a venous catheter.

(BASEC)

Intervention under investigation

No intervention planned

(BASEC)

Disease under investigation

Urea cycle disorders

(BASEC)

Criteria for participation in trial
Healthy Patients with urea cycle defect Written consent (BASEC)

Exclusion criteria
Acute or chronic illness requiring treatment Pregnancy Breastfeeding Intake of N-Carbamylglutamate (if intake cannot be interrupted for 1 day) (BASEC)

Trial sites

Zurich

(BASEC)

Switzerland (ICTRP)

Sponsor

University Children's Hospital Zurich

(BASEC)

Contact

Contact Person Switzerland

Johannes Häberle

+41442495988

johannes.haeberle@kispi.uzh.ch

University Children's Hospital Zutich

(BASEC)

General Information

0041-442667342+41442667342

johannes.haeberle@kispi.uzh.ch

(ICTRP)

Name of the authorising ethics committee (for multicentre studies, only the lead committee)

Ethics Committee Zurich

(BASEC)

Date of authorisation

02.10.2019

(BASEC)


ICTRP Trial ID
NCT05671666 (ICTRP)

Official title (approved by ethics committee)
Ureagenesis analysis in healthy subjects and in urea cycle disorder patients (BASEC)

Academic title
Ureagenesis Analysis in Healthy Subjects and in Urea Cycle Disorder Patients (ICTRP)

Public title
Ureagenesis Analysis in Healthy Subjects and in Urea Cycle Disorder Patients (ICTRP)

Disease under investigation
Urea Cycle Disorders (ICTRP)

Intervention under investigation
Diagnostic Test: Urea cycle flux study (ICTRP)

Type of trial
Interventional (ICTRP)

Trial design
Allocation: N/A. Intervention model: Single Group Assignment. Primary purpose: Diagnostic. Masking: None (Open Label). (ICTRP)

Inclusion/Exclusion criteria
Inclusion Criteria:

- healthy subjects at any age and given written informed consent

- subjects with a UCD confirmed by genetic or enzymatic diagnostics at any age and
given written informed consent

Exclusion Criteria:

- healthy subjects with acute and chronic disease requiring treatment of any kind

- pregnant or lactating women.

- UCD patients with acute and chronic (other than her/his UCD) disease requiring
treatment

- UCD patients in which intake of carglumic acid cannot be stopped for 24 hours prior
to the test (ICTRP)

not available

Primary and secondary end points
Rate of flux through the urea cycle using stable isotopes in healthy subjects and patients, and the change of rate of flux through the urea cycle in patients after an intervention or for follow-up. (ICTRP)

not available

Registration date
not available

Incorporation of the first participant
not available

Secondary sponsors
not available

Additional contacts
Johannes HberleJohannes Haeberle, Johannes.haeberle@kispi.uzh.chjohannes.haeberle@kispi.uzh.ch, 0041-442667342+41442667342 (ICTRP)

Secondary trial IDs
Ureagenesis01352 (ICTRP)

Results-Individual Participant Data (IPD)
not available

Further information on the trial
https://clinicaltrials.gov/ct2/show/NCT05671666 (ICTRP)

Results of the trial

Results summary

not available

Link to the results in the primary register

not available